CASE REPORT |
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Year : 2021 | Volume
: 7
| Issue : 2 | Page : 74-77 |
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Sturge–Weber syndrome
Kalpana Verma, Seema Thakur, Ashish Justa
Department of Pediatric and Preventive Dentistry, H. P. Government Dental College and Hospital, Shimla, Himachal Pradesh, India
Correspondence Address:
Kalpana Verma Room No-310, Department of Pediatric and Preventive Dentistry, H. P. Government Dental College and Hospital, Shimla - 171 001, Himachal Pradesh India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/ijohr.ijohr_25_20
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The Sturge–Weber syndrome (SWS) or encephalotrigeminal angiomatosis is specifically congenital, nonhereditary, and rare condition of unknown etiology. It belongs to a group of disorders collectively known as the phakomatoses (“motherspot” diseases). In its complete tri-symptomatic form, SWS is physically characterized by port-wine stains over the trigeminal area, leptomeningeal angiomas usually over the parieto-occipital region, and eye abnormalities. Clinical manifestation of SWS depends on the affected organs and can include seizures, mental retardation, and glaucoma.
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